TY - JOUR AU - Álvarez González, José Victor AU - Bravo López, Susana Belén AU - García-Vence, M. AU - De Castro López, María José AU - Luzardo, A. AU - Colón Mejeras, Cristobal AU - Tomatsu, S. AU - Otero Espinar, Francisco AU - Couce Pico, María Luz PY - 2019 SN - 1661-6596 UR - http://hdl.handle.net/20.500.11940/15803 AB - Morquio A syndrome, or mucopolysaccharidosis type IVA (MPS IVA), is a lysosomal storage disease due to mutations in the N-acetylgalactosamine-6-sulfatase (GALNS) gene. Systemic skeletal dysplasia and the related clinical features of MPS IVA are due to... LA - eng KW - Adult KW - Humans KW - Chondroitinsulfatases KW - Young Adult KW - Cells KW - Drug Delivery Systems KW - Liposomes KW - Enzyme Replacement Therapy KW - Proteomics KW - Lipids KW - Nanostructures KW - Mucopolysaccharidosis IV TI - Proteomic analysis in morquio a cells treated with immobilized enzymatic replacement therapy on nanostructured lipid systems DO - 10.3390/ijms20184610 T2 - INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES M2 - 4610 KW - CHUS KW - IDIS VL - 20 ER -