TY  - GEN 
AU  - Sánchez Pintos, Paula
AU  - Meavilla, S.
AU  - López-Ramos, M.G.
AU  - García-Cazorla, Á.
AU  - Couce Pico, María Luz
PY  - 2022
SN  - 2296-2360
UR  - http://hdl.handle.net/20.500.11940/20688
AB  - Background: Metabolic decompensation episodes (DEs) in Maple Syrup urine disease (MSUD) result in brain accumulation of toxic branched-chain amino acids (BCAAs) and their respective branched-chain ?-keto acids that could induce neuroinflammation,...
LA  - eng
TI  - Intravenous branched-chain amino-acid-free solution for the treatment of metabolic decompensation episodes in Spanish pediatric patients with maple syrup urine disease
DO  - 10.3389/fped.2022.969741
KW  - AS Santiago
KW  - CHUS
KW  - IDIS
VL  - 10
ER  -